some   cases  of ambiguous genitalia , are very rare and their diagnosis

   and decision on their treatment  methods  are  of  special  importance.

          Our  patient  was  16 – years  old   with   female  appearance ,  had  an

   ambiguous Genitalia ,  2  small  and  atrophic   testes   in   the  internal   ring

   of   inguinal  channel.  Her  chromosomal   karyotype  was  46xy .  Here   we

   describe  and  discuss   our diagnostic  steps , management ,   and surgical 

   vaginoplasty  procedure with using sigmoid.